Chapter IX
Diseases of the circulatory system
(I00-I99)

Other forms of heart disease
(I30-I52)

I30 Acute pericarditis
Includes: acute pericardial effusion
Excludes: rheumatic pericarditis (acute) ( I01.0 )
I30.0 Acute nonspecific idiopathic pericarditis
I30.1 Infective pericarditis
Pericarditis:
· pneumococcal
· purulent
· staphylococcal
· streptococcal
· viral
Pyopericarditis
Use additional code (B95-B97), if desired, to identify infectious agent.
I30.8 Other forms of acute pericarditis
I30.9 Acute pericarditis, unspecified

I31 Other diseases of pericardium
Excludes: current complications following acute myocardial infarction ( I23.- )
postcardiotomy syndrome ( I97.0 )
trauma ( S26.- )
when specified as rheumatic ( I09.2 )
I31.0 Chronic adhesive pericarditis
Accretio cordis
Adherent pericardium
Adhesive mediastinopericarditis
I31.1 Chronic constrictive pericarditis
Concretio cordis
Pericardial calcification
I31.2 Haemopericardium, not elsewhere classified
I31.3 Pericardial effusion (noninflammatory)
Chylopericardium
I31.8 Other specified diseases of pericardium
Epicardial plaques
Focal pericardial adhesions
I31.9 Disease of pericardium, unspecified
Cardiac tamponade
Pericarditis (chronic) NOS

I32* Pericarditis in diseases classified elsewhere
I32.0* Pericarditis in bacterial diseases classified elsewhere
Pericarditis:
· gonococcal ( A54.8+ )
· meningococcal ( A39.5+ )
· syphilitic ( A52.0+ )
· tuberculous ( A18.8+ )
I32.1* Pericarditis in other infectious and parasitic diseases classified elsewhere
I32.8* Pericarditis in other diseases classified elsewhere
Pericarditis (in):
· rheumatoid ( M05.3+ )
· systemic lupus erythematosus ( M32.1+ )
· uraemic ( N18.8+ )

I33 Acute and subacute endocarditis
Excludes: acute rheumatic endocarditis ( I01.1 )
endocarditis NOS ( I38 )
I33.0 Acute and subacute infective endocarditis
Endocarditis (acute)(subacute):
· bacterial
· infective NOS
· lenta
· malignant
· septic
· ulcerative
Use additional code (B95-B97), if desired, to identify infectious agent.
I33.9 Acute endocarditis, unspecified
Endocarditis
Myoendocarditis
Periendocarditis
}
}
}
acute or subacute

I34 Nonrheumatic mitral valve disorders
Excludes: mitral (valve):
· disease ( I05.9 )
· failure ( I05.8 )
· stenosis ( I05.0 )
when of unspecified cause but with mention of:
· diseases of aortic valve ( I08.0 )
· mitral stenosis or obstruction ( I05.0 )
when specified as congenital ( Q23.2 , Q23.3 )
when specified as rheumatic ( I05.- )
I34.0 Mitral (valve) insufficiency
Mitral (valve):
· incompetence
· regurgitation
}
}
NOS or of specified cause, except rheumatic
I34.1 Mitral (valve) prolapse
Floppy mitral valve syndrome
Excludes: Marfan's syndrome ( Q87.4 )
I34.2 Nonrheumatic mitral (valve) stenosis
I34.8 Other nonrheumatic mitral valve disorders
I34.9 Nonrheumatic mitral valve disorder, unspecified

I35 Nonrheumatic aortic valve disorders
Excludes: hypertrophic subaortic stenosis ( I42.1 )
when of unspecified cause but with mention of diseases of mitral valve ( I08.0 )
when specified as congenital ( Q23.0 , Q23.1 )
when specified as rheumatic ( I06.- )
I35.0 Aortic (valve) stenosis
I35.1 Aortic (valve) insufficiency
Aortic (valve):
· incompetence
· regurgitation
}
}
NOS or of specified cause, except rheumatic
I35.2 Aortic (valve) stenosis with insufficiency
I35.8 Other aortic valve disorders
I35.9 Aortic valve disorder, unspecified

I36 Nonrheumatic tricuspid valve disorders
Excludes: when of unspecified cause ( I07.- )
when specified as congenital ( Q22.4 , Q22.8 , Q22.9 )
when specified as rheumatic ( I07.- )
I36.0 Nonrheumatic tricuspid (valve) stenosis
I36.1 Nonrheumatic tricuspid (valve) insufficiency
Tricuspid (valve):
· incompetence
· regurgitation
}
}
of specified cause, except rheumatic
I36.2 Nonrheumatic tricuspid (valve) stenosis with insufficiency
I36.8 Other nonrheumatic tricuspid valve disorders
I36.9 Nonrheumatic tricuspid valve disorder, unspecified

I37 Pulmonary valve disorders
Excludes: when specified as congenital ( Q22.1 , Q22.2 , Q22.3 )
when specified as rheumatic ( I09.8 )
I37.0 Pulmonary valve stenosis
I37.1 Pulmonary valve insufficiency
Pulmonary valve:
· incompetence
· regurgitation
}
}
NOS or of specified cause, except rheumatic
I37.2 Pulmonary valve stenosis with insufficiency
I37.8 Other pulmonary valve disorders
I37.9 Pulmonary valve disorder, unspecified

I38 Endocarditis, valve unspecified
Endocarditis (chronic) NOS
Valvular:
· incompetence
· insufficiency
· regurgitation
· stenosis
Valvulitis (chronic)
}
}
}
}
}
}
of unspecified valve
{
{
NOS or of specified cause, except rheumatic or congenital
Excludes: congenital insufficiency of cardiac valve NOS ( Q24.8 )
congenital stenosis of cardiac valve NOS ( Q24.8 )
endocardial fibroelastosis ( I42.4 )
when specified as rheumatic ( I09.1 )

I39* Endocarditis and heart valve disorders in diseases classified elsewhere
Includes: endocardial involvement in:
· candidal infection ( B37.6+ )
· gonococcal infection ( A54.8+ )
· Libman-Sacks disease ( M32.1+ )
· meningococcal infection ( A39.5+ )
· rheumatoid arthritis ( M05.3+ )
· syphilis ( A52.0+ )
· tuberculosis ( A18.8+ )
· typhoid fever ( A01.0+ )
I39.0* Mitral valve disorders in diseases classified elsewhere
I39.1* Aortic valve disorders in diseases classified elsewhere
I39.2* Tricuspid valve disorders in diseases classified elsewhere
I39.3* Pulmonary valve disorders in diseases classified elsewhere
I39.4* Multiple valve disorders in diseases classified elsewhere
I39.8* Endocarditis, valve unspecified, in diseases classified elsewhere

I40 Acute myocarditis
I40.0 Infective myocarditis
Septic myocarditis
Use additional code (B95-B97), if desired, to identify infectious agent.
I40.1 Isolated myocarditis
I40.8 Other acute myocarditis
I40.9 Acute myocarditis, unspecified

I41* Myocarditis in diseases classified elsewhere
I41.0* Myocarditis in bacterial diseases classified elsewhere
Myocarditis:
· diphtheritic ( A36.8+ )
· gonococcal ( A54.8+ )
· meningococcal ( A39.5+ )
· syphilitic ( A52.0+ )
· tuberculous ( A18.8+ )
I41.1* Myocarditis in viral diseases classified elsewhere
Influenzal myocarditis (acute):
· avian influenza virus identified ( J09+ )
· other virus identified ( J10.8+ )
· virus not identified ( J11.8+ )
Mumps myocarditis ( B26.8+ )
I41.2* Myocarditis in other infectious and parasitic diseases classified elsewhere
Myocarditis in:
· Chagas' disease (chronic) ( B57.2+ )
· acute ( B57.0+ )
· toxoplasmosis ( B58.8+ )
I41.8* Myocarditis in other diseases classified elsewhere
Rheumatoid myocarditis ( M05.3+ )
Sarcoid myocarditis ( D86.8+ )

I42 Cardiomyopathy
Excludes: cardiomyopathy complicating:
· pregnancy ( O99.4 )
· puerperium ( O90.3 )
ischaemic cardiomyopathy ( I25.5 )
I42.0 Dilated cardiomyopathy
Congestive cardiomyopathy
I42.1 Obstructive hypertrophic cardiomyopathy
Hypertrophic subaortic stenosis
I42.2 Other hypertrophic cardiomyopathy
Nonobstructive hypertrophic cardiomyopathy
I42.3 Endomyocardial (eosinophilic) disease
Endomyocardial (tropical) fibrosis
Löffler's endocarditis
I42.4 Endocardial fibroelastosis
Congenital cardiomyopathy
I42.5 Other restrictive cardiomyopathy
Constrictive cardiomyopathy NOS
I42.6 Alcoholic cardiomyopathy
I42.7 Cardiomyopathy due to drugs and other external agents
Use additional external cause code (Chapter XX), if desired, to identify cause.
I42.8 Other cardiomyopathies
I42.9 Cardiomyopathy, unspecified
Cardiomyopathy (primary)(secondary) NOS

I43* Cardiomyopathy in diseases classified elsewhere
I43.0* Cardiomyopathy in infectious and parasitic diseases classified elsewhere
Cardiomyopathy in diphtheria ( A36.8+ )
I43.1* Cardiomyopathy in metabolic diseases
Cardiac amyloidosis ( E85.-+ )
I43.2* Cardiomyopathy in nutritional diseases
Nutritional cardiomyopathy NOS ( E63.9+ )
I43.8* Cardiomyopathy in other diseases classified elsewhere
Gouty tophi of heart ( M10.0+ )
Thyrotoxic heart disease ( E05.9+ )

I44 Atrioventricular and left bundle-branch block
I44.0 Atrioventricular block, first degree
I44.1 Atrioventricular block, second degree
Atrioventricular block, type I and II
Möbitz block, type I and II
Second-degree block, type I and II
Wenckebach's block
I44.2 Atrioventricular block, complete
Complete heart block NOS
Third-degree block
I44.3 Other and unspecified atrioventricular block
Atrioventricular block NOS
I44.4 Left anterior fascicular block
I44.5 Left posterior fascicular block
I44.6 Other and unspecified fascicular block
Left bundle-branch hemiblock NOS
I44.7 Left bundle-branch block, unspecified

I45 Other conduction disorders
I45.0 Right fascicular block
I45.1 Other and unspecified right bundle-branch block
Right bundle-branch block NOS
I45.2 Bifascicular block
I45.3 Trifascicular block
I45.4 Nonspecific intraventricular block
Bundle-branch block NOS
I45.5 Other specified heart block
Sinoatrial block
Sinoauricular block
Excludes: heart block NOS ( I45.9 )
I45.6 Pre-excitation syndrome
Anomalous atrioventricular excitation
Atrioventricular conduction:
· accelerated
· accessory
· pre-excitation
Lown-Ganong-Levine syndrome
Wolff-Parkinson-White syndrome
I45.8 Other specified conduction disorders
Atrioventricular [AV] dissociation
Interference dissociation
I45.9 Conduction disorder, unspecified
Heart block NOS
Stokes-Adams syndrome

I46 Cardiac arrest
Excludes: cardiogenic shock ( R57.0 )
complicating:
· abortion or ectopic or molar pregnancy ( O00-O07 , O08.8 )
· obstetric surgery and procedures ( O75.4 )
I46.0 Cardiac arrest with successful resuscitation
I46.1 Sudden cardiac death, so described
Excludes: sudden death:
· NOS ( R96.- )
· with:
  · conduction disorder ( I44-I45 )
  · myocardial infarction ( I21-I22 )
I46.9 Cardiac arrest, unspecified

I47 Paroxysmal tachycardia
Excludes: complicating:
· abortion or ectopic or molar pregnancy ( O00-O07 , O08.8 )
· obstetric surgery and procedures ( O75.4 )
tachycardia:
· NOS ( R00.0 )
· sinoauricular NOS ( R00.0 )
· sinus [sinusal] NOS ( R00.0 )
I47.0 Re-entry ventricular arrhythmia
I47.1 Supraventricular tachycardia
Paroxysmal tachycardia:
· atrial
· atrioventricular [AV]
· junctional
· nodal
I47.2 Ventricular tachycardia
I47.9 Paroxysmal tachycardia, unspecified
Bouveret(-Hoffmann) syndrome

I48 Atrial fibrillation and flutter

I49 Other cardiac arrhythmias
Excludes: bradycardia:
· NOS ( R00.1)
· sinoatrial ( R00.1)
· sinus ( R00.1)
· vagal ( R00.1)
complicating:
· abortion or ectopic or molar pregnancy ( O00-O07, O08.8)
· obstetric surgery and procedures ( O75.4)
neonatal cardiac dysrhythmia ( P29.1)
I49.0 Ventricular fibrillation and flutter
#I49.00* Ventricular fibrillation and flutter with structural heart diseases
#I49.01* Ventricular fibrillation and flutter without structural heart diseases (idiopathic)
[Brugada's syndrome]
#I49.08* Other ventricular fibrillation and flutter
#I49.09* Ventricular fibrillation and flutter, unspecified
I49.1 Atrial premature depolarization
Atrial premature beats
I49.2 Junctional premature depolarization
I49.3 Ventricular premature depolarization
I49.4 Other and unspecified premature depolarization
Ectopic beats
Extrasystoles
Extrasystolic arrhythmias
Premature:
· beats NOS
· contractions
I49.5 Sick sinus syndrome
Tachycardia-bradycardia syndrome
I49.8 Other specified cardiac arrhythmias
Rhythm disorder:
· coronary sinus
· ectopic
· nodal
I49.9 Cardiac arrhythmia, unspecified
Arrhythmia (cardiac) NOS

I50 Heart failure
Excludes: complicating:
· abortion or ectopic or molar pregnancy ( O00-O07 , O08.8 )
· obstetric surgery and procedures ( O75.4 )
due to hypertension ( I11.0 )
· with renal disease ( I13.- )
following cardiac surgery or due to presence of cardiac prosthesis ( I97.1 )
neonatal cardiac failure ( P29.0 )
I50.0 Congestive heart failure
Congestive heart disease
Right ventricular failure (secondary to left heart failure)
I50.1 Left ventricular failure
Cardiac asthma
Left heart failure
Oedema of lung
Pulmonary oedema
}
}
with mention of heart disease NOS or heart failure
I50.9 Heart failure, unspecified
Cardiac, heart or myocardial failure NOS

I51 Complications and ill-defined descriptions of heart disease
Excludes: any condition in I51.4-I51.9 due to hypertension ( I11.- )
· with renal disease ( I13.- )
complications following acute myocardial infarction ( I23.- )
when specified as rheumatic ( I00-I09 )
I51.0 Cardiac septal defect, acquired
Acquired septal defect (old):
· atrial
· auricular
· ventricular
I51.1 Rupture of chordae tendineae, not elsewhere classified
I51.2 Rupture of papillary muscle, not elsewhere classified
I51.3 Intracardiac thrombosis, not elsewhere classified
Thrombosis (old):
· apical
· atrial
· auricular
· ventricular
I51.4 Myocarditis, unspecified
Myocardial fibrosis
Myocarditis:
· NOS
· chronic (interstitial)
I51.5 Myocardial degeneration
Degeneration of heart or myocardium:
· fatty
· senile
Myocardial disease
I51.6 Cardiovascular disease, unspecified
Cardiovascular accident NOS
Excludes: atherosclerotic cardiovascular disease, so described ( I25.0 )
I51.7 Cardiomegaly
Cardiac:
· dilatation
· hypertrophy
Ventricular dilatation
I51.8 Other ill-defined heart diseases
Carditis (acute)(chronic)
Pancarditis (acute)(chronic)
I51.9 Heart disease, unspecified

I52* Other heart disorders in diseases classified elsewhere
Excludes: cardiovascular disorders NOS in diseases classified elsewhere ( I98.-* )
I52.0* Other heart disorders in bacterial diseases classified elsewhere
Meningococcal carditis NEC ( A39.5+ )
I52.1* Other heart disorders in other infectious and parasitic diseases classified elsewhere
Pulmonary heart disease in schistosomiasis ( B65.-+ )
I52.8* Other heart disorders in other diseases classified elsewhere
Rheumatoid carditis ( M05.3+ )