Chapter IX

Diseases of the circulatory system

Acute rheumatic fever

I00 Rheumatic fever without mention of heart involvement
Arthritis, rheumatic, acute or subacute

I01 Rheumatic fever with heart involvement
Excludes: chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of recrudescence or activity of the rheumatic process. In cases where there is doubt as to rheumatic activity at the time of death refer to the mortality coding rules and guidelines in Volume 2.
I01.0 Acute rheumatic pericarditis
Any condition in I00 with pericarditis
Rheumatic pericarditis (acute)
Excludes: when not specified as rheumatic ( I30.- )
I01.1 Acute rheumatic endocarditis
Any condition in I00 with endocarditis or valvulitis
Acute rheumatic valvulitis
I01.2 Acute rheumatic myocarditis
Any condition in I00 with myocarditis
I01.8 Other acute rheumatic heart disease
Any condition in I00 with other or multiple types of heart involvement
Acute rheumatic pancarditis
I01.9 Acute rheumatic heart disease, unspecified
Any condition in I00 with unspecified type of heart involvement
· carditis, acute
· heart disease, active or acute

I02 Rheumatic chorea
Includes: Sydenham's chorea
Excludes: chorea:
· NOS ( G25.5 )
· Huntington ( G10 )
I02.0 Rheumatic chorea with heart involvement
Chorea NOS with heart involvement
Rheumatic chorea with heart involvement of any type classifiable under I01.-
I02.9 Rheumatic chorea without heart involvement
Rheumatic chorea NOS