Includes: | autoimmune disease:
· NOS · systemic collagen (vascular) disease: · NOS · systemic |
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Excludes: | autoimmune disease, single organ or single cell-type (code to relevant condition category)
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M31 | Other necrotizing vasculopathies | |||||||
M31.0 | Hypersensitivity angiitis | |||||||
Goodpasture's syndrome
|
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M31.1 | Thrombotic microangiopathy | |||||||
Thrombotic thrombocytopenic purpura
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M31.2 | Lethal midline granuloma | |||||||
M31.3 | Wegener's granulomatosis | |||||||
Necrotizing respiratory granulomatosis
|
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M31.4 | Aortic arch syndrome [Takayasu] | |||||||
M31.5 | Giant cell arteritis with polymyalgia rheumatica | |||||||
M31.6 # |
Other giant cell arteritis Temporal arteritis |
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M31.7 | Microscopic polyangiitis | |||||||
Microscopic polyarteritis
|
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Excludes: | polyarteritis nodosa
|
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M31.8 | Other specified necrotizing vasculopathies | |||||||
Hypocomplementaemic vasculitis
|
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M31.9 | Necrotizing vasculopathy, unspecified |
M32 | Systemic lupus erythematosus | |||||||
Excludes: | lupus erythematosus (discoid)(NOS)
|
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M32.0 | Drug-induced systemic lupus erythematosus | |||||||
Use additional external cause code (Chapter XX), if desired, to identify drug. | ||||||||
M32.1+ | Systemic lupus erythematosus with organ or system involvement | |||||||
Libman-Sacks disease
Lupus pericarditis Systemic lupus erythematosus with: · kidney involvement · lung involvement |
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M32.8 | Other forms of systemic lupus erythematosus | |||||||
M32.9 | Systemic lupus erythematosus, unspecified |
M33 | Dermatopolymyositis | |||||||
M33.0 | Juvenile dermatomyositis | |||||||
M33.1 | Other dermatomyositis | |||||||
M33.2 | Polymyositis | |||||||
M33.9 | Dermatopolymyositis, unspecified |
M34 | Systemic sclerosis | |||||||
Includes: | scleroderma
|
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Excludes: | scleroderma:
· circumscribed · neonatal |
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M34.0 | Progressive systemic sclerosis | |||||||
M34.1 | CR(E)ST syndrome | |||||||
Combination of calcinosis, Raynaud's phenomenon, (o)esophageal dysfunction, sclerodactyly, telangiectasia. | ||||||||
M34.2 | Systemic sclerosis induced by drugs and chemicals | |||||||
Use additional external cause code (Chapter XX), if desired, to identify cause. | ||||||||
M34.8 | Other forms of systemic sclerosis | |||||||
Systemic sclerosis with:
· lung involvement+ · myopathy+ |
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M34.9 | Systemic sclerosis, unspecified |
M35 | Other systemic involvement of connective tissue | |||||||
Excludes: | reactive perforating collagenosis
|
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M35.0 | Sicca syndrome [Sjögren] | |||||||
Sjögren's syndrome with:
· keratoconjunctivitis+ · lung involvement+ · myopathy+ · renal tubulo-interstitial disorders+ |
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M35.1 | Other overlap syndromes | |||||||
Mixed connective tissue disease
|
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Excludes: | polyangiitis overlap syndrome
|
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M35.2 | Behçet's disease | |||||||
M35.3 | Polymyalgia rheumatica | |||||||
Excludes: | polymyalgia rheumatica with giant cell arteritis
|
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M35.4 | Diffuse (eosinophilic) fasciitis | |||||||
M35.5 | Multifocal fibrosclerosis | |||||||
M35.6 | Relapsing panniculitis [Weber-Christian] | |||||||
Excludes: | panniculitis:
· NOS · lupus |
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M35.7 | Hypermobility syndrome | |||||||
Familial ligamentous laxity
|
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Excludes: | Ehlers-Danlos syndrome
ligamentous laxity NOS |
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M35.8 | Other specified systemic involvement of connective tissue | |||||||
M35.9 | Systemic involvement of connective tissue, unspecified | |||||||
Autoimmune disease (systemic) NOS
Collagen (vascular) disease NOS |
M36* | Systemic disorders of connective tissue in diseases classified elsewhere | |||||||
Excludes: | arthropathies in diseases classified elsewhere
|
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M36.0* |
Dermato(poly)myositis in neoplastic disease
|
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M36.1* |
Arthropathy in neoplastic disease
|
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Arthropathy in:
· leukaemia · malignant histiocytosis · multiple myeloma |
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M36.2* |
Haemophilic arthropathy
|
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M36.3* |
Arthropathy in other blood disorders
|
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Excludes: | arthropathy in Henoch(-Schönlein) purpura
|
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M36.4* | Arthropathy in hypersensitivity reactions classified elsewhere | |||||||
Arthropathy in Henoch(-Schönlein) purpura
|
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M36.8* | Systemic disorders of connective tissue in other diseases classified elsewhere | |||||||
Systemic disorders of connective tissue in:
· hypogammaglobulinaemia · ochronosis |