Chapter III

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

Coagulation defects, purpura and other haemorrhagic conditions

D65 Disseminated intravascular coagulation [defibrination syndrome]
Afibrinogenaemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation [DIC]
Fibrinolytic haemorrhage, acquired
· fibrinolytic
· fulminans
Excludes: that (complicating):
· abortion or ectopic or molar pregnancy ( O00-O07 , O08.1 )
· in newborn ( P60 )
· pregnancy, childbirth and the puerperium ( O45.0 , O46.0 , O67.0 , O72.3 )

D66 Hereditary factor VIII deficiency
Deficiency factor VIII (with functional defect)
· A
· classical
Excludes: factor VIII deficiency with vascular defect ( D68.0 )

D67 Hereditary factor IX deficiency
Christmas disease
· factor IX (with functional defect)
· plasma thromboplastin component [PTC]
Haemophilia B

D68 Other coagulation defects
Excludes: those complicating:
· abortion or ectopic or molar pregnancy ( O00-O07, O08.1)
· pregnancy, childbirth and the puerperium ( O45.0, O46.0, O67.0, O72.3)
D68.0 Von Willebrand's disease
Factor VIII deficiency with vascular defect
Vascular haemophilia
Excludes: capillary fragility (hereditary) ( D69.8)
factor VIII deficiency:
· NOS ( D66)
· with functional defect ( D66)
D68.1 Hereditary factor XI deficiency
Haemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
D68.2 Hereditary deficiency of other clotting factors
Congenital afibrinogenaemia
· AC globulin
· proaccelerin
Deficiency of factor:
· I [fibrinogen]
· II [prothrombin]
· V [labile]
· VII [stable]
· X [Stuart-Prower]
· XII [Hageman]
· XIII [fibrin-stabilizing]
Dysfibrinogenaemia (congenital)
Owren's disease
D68.3 Haemorrhagic disorder due to circulating anticoagulants
Haemorrhage during long-term use of anticoagulants
Increase in:
· antithrombin
· anti-VIIIa
· anti-IXa
· anti-Xa
· anti-XIa
Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant.
Excludes: long-term use of anticoagulants without haemorrhage (Z92.1)
D68.4 Acquired coagulation factor deficiency
Deficiency of coagulation factor due to:
· liver disease
· vitamin K deficiency
Excludes: vitamin K deficiency of newborn ( P53)
D68.8 Other specified coagulation defects

Inherited hypercoagulable states,deficiencies of antithrombin III,protein-C,protein-S
and factor V-leiden

#D68.81 Acquired hypercoagulable states
Antiphospholipid syndrome
Presence of systemic lupus erythematosus [SLE] inhibitor
#D68.88 Other specified coagulation defects
D68.9 Coagulation defect, unspecified

D69 Purpura and other haemorrhagic conditions
Excludes: benign hypergammaglobulinaemic purpura ( D89.0 )
cryoglobulinaemic purpura ( D89.1 )
essential (haemorrhagic) thrombocythaemia ( D47.3 )
purpura fulminans ( D65 )
thrombotic thrombocytopenic purpura ( M31.1 )
D69.0 Allergic purpura
· anaphylactoid
· Henoch(-Schönlein)
· nonthrombocytopenic:
  · haemorrhagic
  · idiopathic
· vascular
Vasculitis, allergic
D69.1 Qualitative platelet defects
# Acquired platelet dysfunction with eosinophilia
Bernard-Soulier [giant platelet] syndrome
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (haemorrhagic)(hereditary)
Excludes: von Willebrand's disease ( D68.0 )
D69.2 Other nonthrombocytopenic purpura
· senile
· simplex
D69.3 Idiopathic thrombocytopenic purpura
Evans' syndrome
D69.4 Other primary thrombocytopenia
Excludes: thrombocytopenia with absent radius ( Q87.2 )
transient neonatal thrombocytopenia ( P61.0 )
Wiskott-Aldrich syndrome ( D82.0 )
D69.5 Secondary thrombocytopenia
Use additional external cause code (Chapter XX), if desired, to identify cause.
D69.6 Thrombocytopenia, unspecified
D69.8 Other specified haemorrhagic conditions
Capillary fragility (hereditary)
Vascular pseudohaemophilia
D69.9 Haemorrhagic condition, unspecified