Includes: | defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease sarcoidosis |
|||||||
Excludes: | autoimmune disease (systemic) NOS
functional disorders of polymorphonuclear neutrophils human immunodeficiency virus [HIV] disease |
D81 | Combined immunodeficiencies | |||||||
Excludes: | autosomal recessive agammaglobulinaemia (Swiss type)
|
|||||||
D81.0 | Severe combined immunodeficiency [SCID] with reticular dysgenesis | |||||||
D81.1 | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers | |||||||
D81.2 | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers | |||||||
D81.3 | Adenosine deaminase [ADA] deficiency | |||||||
D81.4 | Nezelof's syndrome | |||||||
D81.5 | Purine nucleoside phosphorylase [PNP] deficiency | |||||||
D81.6 | Major histocompatibility complex class I deficiency | |||||||
Bare lymphocyte syndrome
|
||||||||
D81.7 | Major histocompatibility complex class II deficiency | |||||||
D81.8 | Other combined immunodeficiencies | |||||||
Biotin-dependent carboxylase deficiency
|
||||||||
D81.9 | Combined immunodeficiency, unspecified | |||||||
Severe combined immunodeficiency disorder [SCID] NOS
|
D82 | Immunodeficiency associated with other major defects | |||||||
Excludes: | ataxia telangiectasia [Louis-Bar]
|
|||||||
D82.0 | Wiskott-Aldrich syndrome | |||||||
Immunodeficiency with thrombocytopenia and eczema
|
||||||||
D82.1 | Di George's syndrome | |||||||
Pharyngeal pouch syndrome
Thymic: · alymphoplasia · aplasia or hypoplasia with immunodeficiency |
||||||||
D82.2 | Immunodeficiency with short-limbed stature | |||||||
D82.3 | Immunodeficiency following hereditary defective response to Epstein-Barr virus | |||||||
X-linked lymphoproliferative disease
|
||||||||
D82.4 | Hyperimmunoglobulin E [IgE] syndrome | |||||||
D82.8 | Immunodeficiency associated with other specified major defects | |||||||
D82.9 | Immunodeficiency associated with major defect, unspecified |
D86 | Sarcoidosis | |||||||
D86.0 | Sarcoidosis of lung | |||||||
D86.1 | Sarcoidosis of lymph nodes | |||||||
D86.2 | Sarcoidosis of lung with sarcoidosis of lymph nodes | |||||||
D86.3 | Sarcoidosis of skin | |||||||
D86.8 | Sarcoidosis of other and combined sites | |||||||
Iridocyclitis in sarcoidosis+
Multiple cranial nerve palsies in sarcoidosis+ Sarcoid: · arthropathy+ · myocarditis+ · myositis+ Uveoparotid fever [Heerfordt] |
||||||||
D86.9 | Sarcoidosis, unspecified |
D89 | Other disorders involving the immune mechanism, not elsewhere classified | |||||||
Excludes: | hyperglobulinaemia NOS
monoclonal gammopathy transplant failure and rejection |
|||||||
D89.0 | Polyclonal hypergammaglobulinaemia | |||||||
Benign hypergammaglobulinaemic purpura
Polyclonal gammopathy NOS |
||||||||
D89.1 | Cryoglobulinaemia | |||||||
Cryoglobulinaemia:
· essential · idiopathic · mixed · primary · secondary Cryoglobulinaemic: · purpura · vasculitis |
||||||||
D89.2 | Hypergammaglobulinaemia, unspecified | |||||||
D89.8 | Other specified disorders involving the immune mechanism, not elsewhere classified | |||||||
D89.9 | Disorder involving the immune mechanism, unspecified | |||||||
Immune disease NOS
|