Q20 | Congenital malformations of cardiac chambers and connections | |||||||
Excludes: | dextrocardia with situs inversus
mirror-image atrial arrangement with situs inversus |
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Q20.0 | Common arterial trunk | |||||||
Persistent truncus arteriosus
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Q20.1 | Double outlet right ventricle | |||||||
Taussig-Bing syndrome
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Q20.2 | Double outlet left ventricle | |||||||
Q20.3 | Discordant ventriculoarterial connection | |||||||
Dextrotransposition of aorta
Transposition of great vessels (complete) |
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Q20.4 | Double inlet ventricle | |||||||
Common ventricle
Cor triloculare biatriatum Single ventricle |
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Q20.5 | Discordant atrioventricular connection | |||||||
Corrected transposition
Laevotransposition Ventricular inversion |
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Q20.6 | Isomerism of atrial appendages | |||||||
Isomerism of atrial appendages with asplenia or polysplenia
|
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Q20.8 | Other congenital malformations of cardiac chambers and connections | |||||||
Q20.9 | Congenital malformation of cardiac chambers and connections, unspecified |
Q21 | Congenital malformations of cardiac septa | |||||||
Excludes: | acquired cardiac septal defect
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Q21.0 | Ventricular septal defect | |||||||
Q21.1 | Atrial septal defect | |||||||
Coronary sinus defect
Patent or persistent: · foramen ovale · ostium secundum defect (type II) Sinus venosus defect |
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Q21.2 | Atrioventricular septal defect | |||||||
Common atrioventricular canal
Endocardial cushion defect Ostium primum atrial septal defect (type I) |
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Q21.3 | Tetralogy of Fallot | |||||||
Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle. | ||||||||
Q21.4 | Aortopulmonary septal defect | |||||||
Aortic septal defect
Aortopulmonary window |
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Q21.8 | Other congenital malformations of cardiac septa | |||||||
Eisenmenger's defect
Pentalogy of Fallot |
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Excludes: | Eisenmenger's
· complex · syndrome |
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Q21.9 | Congenital malformation of cardiac septum, unspecified | |||||||
Septal (heart) defect NOS
|
Q23 | Congenital malformations of aortic and mitral valves | |||||||
Q23.0 | Congenital stenosis of aortic valve | |||||||
Congenital aortic:
· atresia · stenosis |
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Excludes: | congenital subaortic stenosis
that in hypoplastic left heart syndrome |
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Q23.1 | Congenital insufficiency of aortic valve | |||||||
Bicuspid aortic valve
Congenital aortic insufficiency |
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Q23.2 | Congenital mitral stenosis | |||||||
Congenital mitral atresia
|
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Q23.3 | Congenital mitral insufficiency | |||||||
Q23.4 | Hypoplastic left heart syndrome | |||||||
Atresia, or marked hypoplasia of aortic orifice or valve, with hypoplasia of ascending aorta and defective develop-ment of left ventricle (with mitral valve stenosis or atresia). | ||||||||
Q23.8 | Other congenital malformations of aortic and mitral valves | |||||||
Q23.9 | Congenital malformation of aortic and mitral valves, unspecified |
Q24 | Other congenital malformations of heart | |||||||
Excludes: | endocardial fibroelastosis
|
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Q24.0 | Dextrocardia | |||||||
Excludes: | dextrocardia with situs inversus
isomerism of atrial appendages (with asplenia or polysplenia) mirror-image atrial arrangement with situs inversus |
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Q24.1 | Laevocardia | |||||||
Location of heart in left hemithorax with apex pointing to the left, but with situs inversus of other viscera and defects of the heart, or corrected transposition of great vessels. | ||||||||
Q24.2 | Cor triatriatum | |||||||
Q24.3 | Pulmonary infundibular stenosis | |||||||
Q24.4 | Congenital subaortic stenosis | |||||||
Q24.5 | Malformation of coronary vessels | |||||||
Congenital coronary (artery) aneurysm
|
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Q24.6 | Congenital heart block | |||||||
Q24.8 | Other specified congenital malformations of heart | |||||||
Congenital:
· diverticulum of left ventricle · malformation of: · myocardium · pericardium Malposition of heart Uhl's disease |
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Q24.9 | Congenital malformation of heart, unspecified | |||||||
Congenital:
|
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· anomaly
· disease |
}
} |
NOS of heart
|
Q25 | Congenital malformations of great arteries | |||||||
Q25.0 | Patent ductus arteriosus | |||||||
Patent ductus Botallo
Persistent ductus arteriosus |
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Q25.1 | Coarctation of aorta | |||||||
Coarctation of aorta (preductal)(postductal)
|
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Q25.2 | Atresia of aorta | |||||||
Q25.3 | Stenosis of aorta | |||||||
Supravalvular aortic stenosis
|
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Excludes: | congenital aortic stenosis
|
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Q25.4 | Other congenital malformations of aorta | |||||||
Absence
Aplasia Congenital: · aneurysm · dilatation |
}
} } } } |
of aorta
|
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Aneurysm of sinus of Valsalva (ruptured)
Double aortic arch [vascular ring of aorta] Hypoplasia of aorta Persistent: · convolutions of aortic arch · right aortic arch |
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Excludes: | hypoplasia of aorta in hypoplastic left heart syndrome
|
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Q25.5 | Atresia of pulmonary artery | |||||||
Q25.6 | Stenosis of pulmonary artery | |||||||
Q25.7 | Other congenital malformations of pulmonary artery | |||||||
Aberrant pulmonary artery
|
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Agenesis
Aneurysm, congenital Anomaly Hypoplasia |
}
} } } |
of pulmonary artery
|
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Pulmonary arteriovenous aneurysm
|
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Q25.8 | Other congenital malformations of great arteries | |||||||
Q25.9 | Congenital malformation of great arteries, unspecified |
Q27 | Other congenital malformations of peripheral vascular system | |||||||
Excludes: | anomalies of:
· cerebral and precerebral vessels · coronary vessels · pulmonary artery congenital retinal aneurysm haemangioma and lymphangioma |
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Q27.0 | Congenital absence and hypoplasia of umbilical artery | |||||||
Single umbilical artery
|
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Q27.1 | Congenital renal artery stenosis | |||||||
Q27.2 | Other congenital malformations of renal artery | |||||||
Congenital malformation of renal artery NOS
Multiple renal arteries |
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Q27.3 | Peripheral arteriovenous malformation | |||||||
Arteriovenous aneurysm
|
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Excludes: | acquired arteriovenous aneurysm
|
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Q27.4 | Congenital phlebectasia | |||||||
Q27.8 | Other specified congenital malformations of peripheral vascular system | |||||||
Aberrant subclavian artery
|
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Absence
Atresia |
}
} |
of artery or vein NEC
|
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Congenital:
· aneurysm (peripheral) · stricture, artery · varix |
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Q27.9 | Congenital malformation of peripheral vascular system, unspecified | |||||||
Anomaly of artery or vein NOS
|
Q28 | Other congenital malformations of circulatory system | |||||||
Excludes: | congenital aneurysm:
· NOS · coronary · peripheral · pulmonary · retinal ruptured: · cerebral arteriovenous malformation · malformation of precerebral vessels |
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Q28.0 | Arteriovenous malformation of precerebral vessels | |||||||
Congenital arteriovenous precerebral aneurysm (nonruptured)
|
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Q28.1 | Other malformations of precerebral vessels | |||||||
Congenital:
· malformation of precerebral vessels NOS · precerebral aneurysm (nonruptured) |
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Q28.2 | Arteriovenous malformation of cerebral vessels | |||||||
Arteriovenous malformation of brain NOS
Congenital arteriovenous cerebral aneurysm (nonruptured) |
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Q28.3 | Other malformations of cerebral vessels | |||||||
Congenital:
· cerebral aneurysm (nonruptured) · malformation of cerebral vessels NOS |
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Q28.8 | Other specified congenital malformations of circulatory system | |||||||
Congenital aneurysm, specified site NEC
|
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Q28.9 | Congenital malformation of circulatory system, unspecified |