Chapter XII

Diseases of the skin and subcutaneous tissue
(L00-L99)

Bullous disorders
(L10-L14)

Excludes: benign familial pemphigus [Hailey-Hailey] ( Q82.8 )
staphylococcal scalded skin syndrome ( L00 )
toxic epidermal necrolysis [Lyell] ( L51.2 )

L10 Pemphigus
Excludes: pemphigus neonatorum ( L00)
L10.0 Pemphigus vulgaris
L10.1 Pemphigus vegetans
L10.2 Pemphigus foliaceus
L10.3 Brazilian pemphigus [fogo selvagem]
L10.4 Pemphigus erythematosus
Senear-Usher syndrome
L10.5 Drug-induced pemphigus
Use additional external cause code (Chapter XX), if desired, to identify drug.
#L10.6 Paraneoplastic pemphigus
L10.8 Other pemphigus
L10.9 Pemphigus, unspecified

L11 Other acantholytic disorders
L11.0 Acquired keratosis follicularis
Excludes: keratosis follicularis (congenital) [Darier-White] ( Q82.8 )
L11.1 Transient acantholytic dermatosis [Grover]
L11.8 Other specified acantholytic disorders
L11.9 Acantholytic disorder, unspecified

L12 Pemphigoid
Excludes: herpes gestationis ( O26.4 )
impetigo herpetiformis ( L40.1 )
L12.0 Bullous pemphigoid
L12.1 Cicatricial pemphigoid
Benign mucous membrane pemphigoid
L12.2 Chronic bullous disease of childhood
Juvenile dermatitis herpetiformis
L12.3 Acquired epidermolysis bullosa
Excludes: epidermolysis bullosa (congenital) ( Q81.- )
L12.8 Other pemphigoid
L12.9 Pemphigoid, unspecified

L13 Other bullous disorders
L13.0 Dermatitis herpetiformis
Duhring's disease
  Excludes:       stomatitis herpetiformis (K12.02 )
L13.1 Subcorneal pustular dermatitis
Sneddon-Wilkinson disease
L13.8 Other specified bullous disorders
L13.9 Bullous disorder, unspecified

L14* Bullous disorders in diseases classified elsewhere