Chapter X

Diseases of the respiratory system
(J00-J99)

Other respiratory diseases principally affecting the interstitium
(J80-J84)

J80 Adult respiratory distress syndrome
Adult hyaline membrane disease

J81 Pulmonary oedema
Acute oedema of lung
Pulmonary congestion (passive)
Excludes: hypostatic pneumonia ( J18.2 )
pulmonary oedema:
· chemical (acute) ( J68.1 )
· due to external agents ( J60-J70 )
· with mention of heart disease NOS or heart failure ( I50.1 )

J82 Pulmonary eosinophilia, not elsewhere classified
Eosinophilic asthma
Löffler's pneumonia
Tropical (pulmonary) eosinophilia NOS
Excludes: due to:
· aspergillosis ( B44.- )
· drugs ( J70.2-J70.4 )
· specified parasitic infection ( B50-B83 )
· systemic connective tissue disorders ( M30-M36 )

J84 Other interstitial pulmonary diseases
Excludes: drug-induced interstitial lung disorders ( J70.2-J70.4 )
interstitial emphysema ( J98.2 )
lung diseases due to external agents ( J60-J70 )
lymphoid interstitial pneumonitis resulting from human immunodeficiency virus [HIV] disease ( B22.1 )
J84.0 Alveolar and parietoalveolar conditions
Alveolar proteinosis
Pulmonary alveolar microlithiasis
J84.1 Other interstitial pulmonary diseases with fibrosis
Diffuse pulmonary fibrosis
Fibrosing alveolitis (cryptogenic)
Hamman-Rich syndrome
Idiopathic pulmonary fibrosis
Excludes: pulmonary fibrosis (chronic):
· due to inhalation of chemicals, gases, fumes or vapours ( J68.4 )
· following radiation ( J70.1 )
J84.8 Other specified interstitial pulmonary diseases
J84.9 Interstitial pulmonary disease, unspecified
Interstitial pneumonia NOS