Q00 | Anencephaly and similar malformations | |||||||
Q00.0 | Anencephaly | |||||||
Acephaly
Acrania Amyelencephaly Hemianencephaly Hemicephaly |
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Q00.1 | Craniorachischisis | |||||||
Q00.2 | Iniencephaly |
Q01 | Encephalocele | |||||||
Includes: | encephalomyelocele
hydroencephalocele hydromeningocele, cranial meningocele, cerebral meningoencephalocele |
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Excludes: | Meckel-Gruber syndrome
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Q01.0 | Frontal encephalocele | |||||||
Q01.1 | Nasofrontal encephalocele | |||||||
Q01.2 | Occipital encephalocele | |||||||
Q01.8 | Encephalocele of other sites | |||||||
Q01.9 | Encephalocele, unspecified |
Q02 | Microcephaly | |||||||
Hydromicrocephaly
Micrencephalon |
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Excludes: | Meckel-Gruber syndrome
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Q03 | Congenital hydrocephalus | |||||||
Includes: | hydrocephalus in newborn
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Excludes: | Arnold-Chiari syndrome
hydrocephalus: · acquired · due to congenital toxoplasmosis · with spina bifida |
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Q03.0 | Malformations of aqueduct of Sylvius | |||||||
Aqueduct of Sylvius:
· anomaly · obstruction, congenital · stenosis |
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Q03.1 | Atresia of foramina of Magendie and Luschka | |||||||
Dandy-Walker syndrome
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Q03.8 | Other congenital hydrocephalus | |||||||
Q03.9 | Congenital hydrocephalus, unspecified |
Q04 | Other congenital malformations of brain | |||||||
Excludes: | cyclopia
macrocephaly |
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Q04.0 | Congenital malformations of corpus callosum | |||||||
Agenesis of corpus callosum
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Q04.1 | Arhinencephaly | |||||||
Q04.2 | Holoprosencephaly | |||||||
Q04.3 | Other reduction deformities of brain | |||||||
Absence
Agenesis Aplasia Hypoplasia |
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of part of brain
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Agyria
Hydranencephaly Lissencephaly Microgyria Pachygyria |
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Excludes: | congenital malformations of corpus callosum
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Q04.4 | Septo-optic dysplasia | |||||||
Q04.5 | Megalencephaly | |||||||
Q04.6 | Congenital cerebral cysts | |||||||
Porencephaly
Schizencephaly |
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Excludes: | acquired porencephalic cyst
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Q04.8 | Other specified congenital malformations of brain | |||||||
Macrogyria
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Q04.9 | Congenital malformation of brain, unspecified | |||||||
Congenital:
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· anomaly
· deformity · disease or lesion · multiple anomalies |
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NOS of brain
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Q05 | Spina bifida | |||||||
Includes: | hydromeningocele (spinal)
meningocele (spinal) meningomyelocele myelocele myelomeningocele rachischisis spina bifida (aperta)(cystica) syringomyelocele |
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Excludes: | Arnold-Chiari syndrome
spina bifida occulta |
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Q05.0 | Cervical spina bifida with hydrocephalus | |||||||
Q05.1 | Thoracic spina bifida with hydrocephalus | |||||||
Spina bifida:
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· dorsal
· thoracolumbar |
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with hydrocephalus
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Q05.2 | Lumbar spina bifida with hydrocephalus | |||||||
Lumbosacral spina bifida with hydrocephalus
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Q05.3 | Sacral spina bifida with hydrocephalus | |||||||
Q05.4 | Unspecified spina bifida with hydrocephalus | |||||||
Q05.5 | Cervical spina bifida without hydrocephalus | |||||||
Q05.6 | Thoracic spina bifida without hydrocephalus | |||||||
Spina bifida:
· dorsal NOS · thoracolumbar NOS |
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Q05.7 | Lumbar spina bifida without hydrocephalus | |||||||
Lumbosacral spina bifida NOS
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Q05.8 | Sacral spina bifida without hydrocephalus | |||||||
Q05.9 | Spina bifida, unspecified |
Q07 | Other congenital malformations of nervous system | |||||||
Excludes: | familial dysautonomia [Riley-Day]
neurofibromatosis (nonmalignant) |
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Q07.0 | Arnold-Chiari syndrome | |||||||
Q07.8 | Other specified congenital malformations of nervous system | |||||||
Agenesis of nerve
Displacement of brachial plexus Jaw-winking syndrome Marcus Gunn's syndrome |
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Q07.9 | Congenital malformation of nervous system, unspecified | |||||||
Congenital:
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· anomaly
· deformity · disease or lesion |
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NOS of nervous system
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