D55 | Anaemia due to enzyme disorders | |||||||
Excludes: | drug-induced enzyme deficiency anaemia
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D55.0 | Anaemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency | |||||||
Favism
G6PD deficiency anaemia |
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D55.1 | Anaemia due to other disorders of glutathione metabolism | |||||||
Anaemia (due to):
· enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway · haemolytic nonspherocytic (hereditary), type I |
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D55.2 | Anaemia due to disorders of glycolytic enzymes | |||||||
Anaemia:
· haemolytic nonspherocytic (hereditary), type II · hexokinase deficiency · pyruvate kinase [PK] deficiency · triose-phosphate isomerase deficiency |
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D55.3 | Anaemia due to disorders of nucleotide metabolism | |||||||
D55.8 | Other anaemias due to enzyme disorders | |||||||
D55.9 | Anaemia due to enzyme disorder, unspecified |
D56 | Thalassaemia | |||||||
D56.0 # |
Alpha thalassaemia
Haemoglobin H disease |
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Excludes: | hydrops fetalis due to haemolytic disease
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D56.1 | Beta thalassaemia | |||||||
# | Beta thalassaemia/haemoglobin E | |||||||
@ |
Cooley's anaemia
Severe beta thalassaemia Sickle-cell beta thalassaemia Thalassaemia: · intermedia · major |
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D56.2 | Delta-beta thalassaemia | |||||||
D56.3 | Thalassaemia trait | |||||||
D56.4 | Hereditary persistence of fetal haemoglobin [HPFH] | |||||||
D56.8 | Other thalassaemias | |||||||
D56.9 | Thalassaemia, unspecified | |||||||
Mediterranean anaemia (with other haemoglobinopathy)
Thalassaemia (minor)(mixed)(with other haemoglobinopathy) |
D57 | Sickle-cell disorders | |||||||
@ |
Excludes: | other haemoglobinopathies
sickle-cell eta thalassaemia (D56.1) |
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D57.0 | Sickle-cell anaemia with crisis | |||||||
Hb-SS disease with crisis
|
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D57.1 | Sickle-cell anaemia without crisis | |||||||
Sickle-cell:
|
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· anaemia
· disease · disorder |
}
} } |
NOS
|
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D57.2 | Double heterozygous sickling disorders | |||||||
Disease:
· Hb-SC · Hb-SD · Hb-SE · sickle-cell thalassaemia |
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D57.3 | Sickle-cell trait | |||||||
Hb-S trait
Heterozygous haemoglobin S |
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D57.8 | Other sickle-cell disorders |
D58 | Other hereditary haemolytic anaemias | |||||||
D58.0 | Hereditary spherocytosis | |||||||
Acholuric (familial) jaundice
Congenital (spherocytic) haemolytic icterus Minkowski-Chauffard syndrome |
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D58.1 | Hereditary elliptocytosis | |||||||
Elliptocytosis (congenital)
Ovalocytosis (congenital)(hereditary) |
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D58.2 | Other haemoglobinopathies | |||||||
Abnormal haemoglobin NOS
Congenital Heinz body anaemia Disease: · Hb-C · Hb-D · Hb-E Haemoglobinopathy NOS Unstable haemoglobin haemolytic disease |
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Excludes: | familial polycythaemia
Hb-M disease hereditary persistence of fetal haemoglobin [HPFH] high-altitude polycythaemia methaemoglobinaemia |
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D58.8 | Other specified hereditary haemolytic anaemias | |||||||
Stomatocytosis
|
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D58.9 | Hereditary haemolytic anaemia, unspecified |
D59 | Acquired haemolytic anaemia | |||||||||
D59.0 | Drug-induced autoimmune haemolytic anaemia | |||||||||
Use additional external cause code (Chapter XX), if desired, to identify drug. | ||||||||||
D59.1 | Other autoimmune haemolytic anaemias | |||||||||
Autoimmune haemolytic disease (cold type)(warm type)
Chronic cold haemagglutinin disease Cold agglutinin: · disease · haemoglobinuria Haemolytic anaemia: · cold type (secondary)(symptomatic) · warm type (secondary)(symptomatic) |
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Excludes: | Evans' syndrome
haemolytic disease of fetus and newborn paroxysmal cold haemoglobinuria |
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D59.2 | Drug-induced nonautoimmune haemolytic anaemia | |||||||||
Drug-induced enzyme deficiency anaemia
|
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Use additional external cause code (Chapter XX), if desired, to identify drug. | ||||||||||
D59.3 | Haemolytic-uraemic syndrome | |||||||||
D59.4 |
Other nonautoimmune haemolytic anaemias |
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Use additional external cause code (Chapter XX), if desired, to identify cause. | ||||||||||
#D59.40 | Chemical
|
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#D59.41 | Infectious | |||||||||
#D59.42 | Microangiopathic | |||||||||
#D59.43 | Physical
|
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#D59.48 | Other nonautoimmune haemolytic anaemias | |||||||||
D59.5 | Paroxysmal nocturnal haemoglobinuria [Marchiafava-Micheli] | |||||||||
Excludes: | haemoglobinuria NOS
|
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D59.6 | Haemoglobinuria due to haemolysis from other external causes | |||||||||
Haemoglobinuria:
· from exertion · march · paroxysmal cold |
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Use additional external cause code (Chapter XX), if desired, to identify cause. | ||||||||||
Excludes: | haemoglobinuria NOS
|
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D59.8 | Other acquired haemolytic anaemias | |||||||||
D59.9 | Acquired haemolytic anaemia, unspecified | |||||||||
Idiopathic haemolytic anaemia, chronic
|