Chapter XVII

Congenital malformations, deformations and chromosomal abnormalities

Congenital malformations of the respiratory system

Q30 Congenital malformations of nose
Excludes: congenital deviation of nasal septum ( Q67.4 )
Q30.0 Choanal atresia
Congenital stenosis
of nares (anterior)(posterior)
Q30.1 Agenesis and underdevelopment of nose
Congenital absence of nose
Q30.2 Fissured, notched and cleft nose
Q30.3 Congenital perforated nasal septum
Q30.8 Other congenital malformations of nose
Accessory nose
Congenital anomaly of nasal sinus wall
Q30.9 Congenital malformation of nose, unspecified

Q31 Congenital malformations of larynx
Excludes: congenital (laryngeal) stridor NOS ( P28.8)
Q31.0 Web of larynx
Web of larynx:
· glottic
· subglottic
Q31.1 Congenital subglottic stenosis
Q31.2 Laryngeal hypoplasia
Q31.3 Laryngocele
@Q31.4 Congenital laryngeal stridor
Q31.5 Congenital laryngomalacia
Q31.8 Other congenital malformations of larynx
of cricoid cartilage, epiglottis, glottis, larynx or thyroid cartilage
Cleft thyroid cartilage
Congenital stenosis of larynx NEC
Fissure of epiglottis
Posterior cleft of cricoid cartilage
Q31.9 Congenital malformation of larynx, unspecified

Q32 Congenital malformations of trachea and bronchus
Excludes: congenital bronchiectasis ( Q33.4 )
Q32.0 Congenital tracheomalacia
Q32.1 Other congenital malformations of trachea
Anomaly of tracheal cartilage
Atresia of trachea
· dilatation
· malformation
· stenosis
of trachea
· tracheocele
Q32.2 Congenital bronchomalacia
Q32.3 Congenital stenosis of bronchus
Q32.4 Other congenital malformations of bronchus
Congenital malformation NOS
of bronchus

Q33 Congenital malformations of lung
Q33.0 Congenital cystic lung
· honeycomb lung
· lung disease:
  · cystic
  · polycystic
Excludes: cystic lung disease, acquired or unspecified ( J98.4 )
Q33.1 Accessory lobe of lung
Q33.2 Sequestration of lung
Q33.3 Agenesis of lung
Absence of lung (lobe)
Q33.4 Congenital bronchiectasis
Q33.5 Ectopic tissue in lung
Q33.6 Hypoplasia and dysplasia of lung
Excludes: pulmonary hypoplasia associated with short gestation ( P28.0 )
Q33.8 Other congenital malformations of lung
Q33.9 Congenital malformation of lung, unspecified

Q34 Other congenital malformations of respiratory system
Q34.0 Anomaly of pleura
Q34.1 Congenital cyst of mediastinum
Q34.8 Other specified congenital malformations of respiratory system
Atresia of nasopharynx
Q34.9 Congenital malformation of respiratory system, unspecified
· absence
· anomaly NOS
of respiratory organ